OXALOSE PRIMÁRIA DIAGNOSTICADA APÓS TRANSPLANTE RENAL - RELATO DE CASO

Authors

  • José Bruno de Almeida Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Kellen Micheline Alves Henrique Costa Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Raquel Martins e Quinino Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Luiz Antônio Ribeiro de Moura Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Ricardo Humberto de Miranda Félix Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Rodrigo de Lima Bandeira Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.
  • Maurício Ferreira da Silva Júnior Universidade Federal do Rio Grande do Norte - Hospital Universitário Onofre Lopes. Centro de Ciências da Saúde, Departamento de Medicina Integrada - Natal/RN – Brasil.

DOI:

https://doi.org/10.53855/bjt.v10i3.343

Keywords:

Hyperoxaluria, Primary , Renal Insufficiency, Kidney Transplantation

Abstract

It is reported a probable case of type 1 primary hyperoxaluria (PH1) in a female young patient whose diagnosis was performed only after the renal transplantation. The purpose of this report is to draw the attention to a rare disease, with hard diagnosis, especially in a patient on substutive renal therapy. The case is related to a 16 years old teenager, on hemodialysis, who was submitted to a living-related donor kidney transplantation (mother), initially presenting a good graft response, with a 1.2mg/dl serum creatinine in the 2nd post-operative day (POD), but developing a progressive and rapid deterioration of the renal function in the 4th POD. A kidney biopsy was performed, and primary oxalosis was diagnosed. Despite the pirydoxine treatment and daily dialysis, the allograft was lost. Definitive treatment of PH1 consists in liver-kidney-transplantation, which must be performed as soon as possible. The knowledgement of such disease among nephrologists is relevant, once patients might be better prepared to renal transplantation, in case the patient is admitted in the ambulatory with this diagnosis.

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Published

2007-06-01

How to Cite

Almeida, J. B. de, Costa, K. M. A. H., Quinino, R. M. e, Moura, L. A. R. de, Félix, R. H. de M., Bandeira, R. de L., & Silva Júnior, M. F. da. (2007). OXALOSE PRIMÁRIA DIAGNOSTICADA APÓS TRANSPLANTE RENAL - RELATO DE CASO. Brazilian Journal of Transplantation, 10(3), 779–781. https://doi.org/10.53855/bjt.v10i3.343

Issue

Section

Case Report