Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report

Authors

  • Marcelo A. F. Ribeiro Jr Beneficência Portuguesa and São Luiz Hospitals – Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Christian Evangelista Garcia Beneficência Portuguesa and São Luiz Hospitals – Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Telma Eugênio dos Santos Beneficência Portuguesa and São Luiz Hospitals – Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Adavio de Oliveira e Silva Beneficência Portuguesa and São Luiz Hospitals – Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Regina Leitão Beneficência Portuguesa and São Luiz Hospitals – Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Cristiane Maria de Freitas Ribeiro Beneficência Portuguesa and São Luiz Hospitals– Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Alexandre Zanchenko Fonseca Beneficência Portuguesa and São Luiz Hospitals– Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Camila de Grande Cambiaghi Beneficência Portuguesa and São Luiz Hospitals– Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Paulo Roberto de Arruda Zantut Beneficência Portuguesa and São Luiz Hospitals– Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.
  • Luiz Augusto Carneiro D’Albuquerque Beneficência Portuguesa and São Luiz Hospitals– Division of Liver Surgery and Transplantation – São Paulo – SP – Brazil.

DOI:

https://doi.org/10.53855/bjt.v8i4.383

Keywords:

Hemangioendothelioma Epithelioid, Liver, Surgery, Transplantation

Abstract

Introduction: Epithelioid hemangioendothelioma of liver is a rare, low-grade neoplasm of vascular origin that has an unpredictable malignant potential. It preferentially arises in soft tissues and bones, and seldom in the liver. Biologically, it trends to be multi-focal and often unresectable. Objective: The outcome of a patient submitted to a living-related liver transplant to treat epithelioid hemangioendothelioma of the liver. Case report: The reported case involves a 39-year old female patient with an immense epithelioid hemangioendothelioma of the liver, involving segments III, IV, V, VII, and VIIl. The prognostic to any kind of treatment was considered unfavorable, and the decision of submitting her to a liver transplant was made. It was suggested a living-related liver transplant. The donor was the patient’s 36-year old brother, who donated his right liver lobe (segments V, VI, VII, VIII). The recipient´s original liver was large, presenting very solid consistence and no node evidence. The transplant itself was performed using the conventional living-related liver transplantation technique. The recovery was good, and she was discharged from hospital on the 15th postoperative day using micophenolate mofetil, tacrolimus, and corticoid. Conclusion: Liver transplantation for epithelioid hemangioendothelioma of the liver can be performed with acceptable survival rate. The living related liver transplant opens a great perspective to that group of patients presenting liver tumors and who are unfeasible to wait for an organ on a waiting list.

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Published

2005-09-01

How to Cite

Ribeiro Jr, M. A. F., Garcia, C. E., Santos, T. E. dos, Silva , A. de O. e, Leitão , R., Ribeiro, C. M. de F., Fonseca, A. Z., Cambiaghi, C. de G., Zantut, P. R. de A., & D’Albuquerque, L. A. C. (2005). Living-related liver transplant to treat epithelioid hemangioendothelioma – a case report. Brazilian Journal of Transplantation, 8(4), 449–451. https://doi.org/10.53855/bjt.v8i4.383

Issue

Section

Case Report